Executive Summary of the Consensus Document on the Diagnosis and Management of Patients with Primary Immunodeficiencies



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Cordero, Elisa and Goycochea Valdivia, Walter and Mendez Echevarría, Ana and M. Allende, Luis and Alsina, Laia and Bravo García Morato, María and Gil Herrera, Juana and Gudiol, Carlota and Len Abad, Óscar and López Medrano, Francisco and Moreno Pérez, David and Muñoz, Patricia and Olbrich, Peter and Sánchez Ramón, Silvia María and Soler Paracín, Pere and Aguilera Cros, Clara and Arostegui, Juan Ignacio and Badell Serra, Isabel and Carbone, Javier and Fortún, Jesús and González Granado, Luis Ignacio and López Granados, Eduardo and Lucena, José Manuel and Parody, Rocío and Ramakers, Jan and Regueiro González-Barros, José Ramón and Rivière, Jacque G and Roca Oporto, Cristina and Rodríguez Pena, Rebeca and Santos Pérez, Juan Luis and Rodríguez Gallego, Carlos and Neth, Olaf (2020) Executive Summary of the Consensus Document on the Diagnosis and Management of Patients with Primary Immunodeficiencies. The Journal of Allergy and Clinical Immunology: In Practice, 8 (10). pp. 3342-3347. ISSN 2213-2198

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Official URL: https://doi.org/10.1016/j.jaip.2020.05.008


Primary immunodeficiencies (PIDs) are rare, undiagnosed and potentially fatal diseases. Clinical manifestations of PID can be fatal or leave sequelae that worsen the quality of life of patients. Traditionally, the treatment of PIDs has been largely supportive, with the exception of bone marrow transplantation and, more recently, gene therapy. The discovering of new affected pathways, the development of new molecules and biologics, and the increasing understanding of the molecular basis of these disorders have created opportunities in PIDs therapy. This document aims to review current knowledge and to provide recommendations about the diagnosis and clinical management of adults and childre with PIDs based on the available scientific evidence taking in to account current practice and future challenges. A systematic review was conducted, and evidence levels based on the available literature are given for each recommendation where available. � 2020 American Academy of Allergy, Asthma & Immunology; Sociedad Española de Enfermedades Infecciosas y Microbiología Clínica [Published by Elsevier Inc./Elsevier Espana]. All rights reserved.

Item Type:Article
Uncontrolled Keywords:Primary immunodeficiencies, Vaccination, Treatment, Haematopoietic progenitors transplantation, Antibiotics
Subjects:Medical sciences > Medicine > Immunology
Medical sciences > Medicine > Oncology
ID Code:69179
Deposited On:16 Dec 2021 10:00
Last Modified:16 Dec 2021 10:00

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